A longitudinal multi-omic dataset of pediatric cystic fibrosis patients receiving lumacaftor/ivacaftor therapy: clinical, microbiome, inflammatory and metabolomic measurements collected over 24 months
Authors
- Rebecca Luise Knoll
- Virginia Rossow
- Juliane Rössler
- Katja Hilbert
- Víctor Hugo Jarquín-Díaz
- Theda Ulrike Patricia Bartolomaeus
- Oliver Nitsche
- Morgan Essex
- Ulrike Löber
- Chen Meng
- Karin Kleigrewe
- Stephan Gehring
- Sofia Kirke Forslund-Startceva
- Krystyna Poplawska
Journal
- Data in Brief
Citation
- Data Brief 69: 113237
Abstract
This article describes a longitudinal multiomic dataset gen- erated within a prospective phase IV pilot study of eight children with cystic fibrosis homozygous for the F508del mutation who initiated lumacaftor/ivacaftor therapy. Partic- ipants were followed for up to 24 months with repeated col- lection of clinical metadata, anthropometric measurements, sweat chloride concentrations, lung function assessments, in- flammatory markers, conventional microbiology results, stool samples, respiratory samples, and serum metabolomics. The resulting dataset links host phenotypes, microbiome compo- sition, inflammatory parameters, and metabolomic measure- ments across multiple body sites and time points. Micro- biome data were generated from stool, sputum and throat swab samples using 16S rRNA gene sequencing, while serum metabolomics was assessed using untargeted mass spectrom- etry. The dataset is publicly available through SRA, MassIVE and GitHub repositories and may support future studies of longitudinal host–microbiome interactions, biomarker discov- ery, methodological benchmarking and comparative analyses across CFTR modulator eras.